साँचा:Amino acid metabolism enzymes देवासंMetabolism: amino acid metabolism · synthesis and catabolism enzymes (essential in CAPS)K→acetyl-CoALYSINE→Saccharopine dehydrogenase · Glutaryl-CoA dehydrogenaseLEUCINE→Branched chain aminotransferase · Branched-chain alpha-keto acid dehydrogenase complex · Isovaleryl coenzyme A dehydrogenase · Methylcrotonyl-CoA carboxylase · Methylglutaconyl-CoA hydratase · 3-hydroxy-3-methylglutaryl-CoA lyaseTRYPTOPHAN→Indoleamine 2,3-dioxygenase/Tryptophan 2,3-dioxygenase · Arylformamidase · Kynureninase · 3-hydroxyanthranilate oxidase · Aminocarboxymuconate-semialdehyde decarboxylase · Aminomuconate-semialdehyde dehydrogenasePHENYLALANINE→tyrosine→(see below)GG→pyruvate→citrateglycine→serine→Serine hydroxymethyltransferase · Serine dehydratase glycine→creatine: Guanidinoacetate N-methyltransferase · Creatine kinasealanine→Alanine transaminasecysteine→D-cysteine desulfhydrasethreonine→L-threonine dehydrogenaseG→glutamate→α-ketoglutarateHISTIDINE→Histidine ammonia-lyase · Urocanate hydratase · Formiminotransferase cyclodeaminaseproline→Proline oxidase · Pyrroline-5-carboxylate reductase · 1-Pyrroline-5-carboxylate dehydrogenase/ALDH4A1 · PYCR1arginine→Ornithine aminotransferase · Ornithine decarboxylase · Agmatinase→alpha-ketoglutarate→TCAGlutamate dehydrogenaseOthercysteine+glutamate→glutathione: Gamma-glutamylcysteine synthetase · Glutathione synthetase · Gamma-glutamyl transpeptidase glutamate→glutamine: Glutamine synthetase · GlutaminaseG→propionyl-CoA→succinyl-CoAVALINE→Branched chain aminotransferase · Branched-chain alpha-keto acid dehydrogenase complex · Enoyl-CoA hydratase · 3-hydroxyisobutyryl-CoA hydrolase · 3-hydroxyisobutyrate dehydrogenase · Methylmalonate semialdehyde dehydrogenaseISOLEUCINE→Branched chain aminotransferase · Branched-chain alpha-keto acid dehydrogenase complex · 3-hydroxy-2-methylbutyryl-CoA dehydrogenaseMETHIONINE→generation of homocysteine: Methionine adenosyltransferase · Adenosylhomocysteinase regeneration of methionine: Methionine synthase/Homocysteine methyltransferase · Betaine-homocysteine methyltransferase conversion to cysteine: Cystathionine beta synthase · Cystathionine gamma-lyaseTHREONINE→Threonine aldolase→succinyl-CoA→TCAPropionyl-CoA carboxylase · Methylmalonyl CoA epimerase · Methylmalonyl-CoA mutaseG→fumaratePHENYLALANINE→tyrosine→Phenylalanine hydroxylase · Tyrosine aminotransferase · 4-Hydroxyphenylpyruvate dioxygenase · Homogentisate 1,2-dioxygenase · Fumarylacetoacetate hydrolase tyrosine→melanin: TyrosinaseG→oxaloacetateasparagine→aspartate→Asparaginase/Asparagine synthetase · Aspartate transaminase M: MET mt, a/u/y/n/h, r/g/c/p/i, f/s/l/o, m au/y/n/h, rgcp/i, f/s/l/o, m, epon meds(A16, C10),intm(a/u/y/n/h, r/g/c/p/i, f/s/o)
